Volume 12, Issue 1, Pages 38-45 (February 2003)

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ABSTRACT

ABSTRACT + REFS

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Central hypoventilation and diaphragmatic eventration: Diagnosis and management☆

Abstract

Congenital central alveolar hypoventilation syndrome (CCAHS) is a disorder of ventilatory control that occurs without neuromuscular blockade or pulmonary disease. It is characterized by a lack of response to habitual respiratory stimulants, especially hypercapnia. In this article, the management of this syndrome by diaphragmatic pacing is discussed. Paralysis of the phrenic nerve in small children usually results from injury during birth or during a cardiothoracic operation and results in eventration of the hemidiaphragm. Alternatively, eventration of the diaphragm may be a congenital condition. In both cases it may lead to respiratory distress in the newborn. In this article, we review the diagnosis of these conditions and their management, focusing on the surgical indications. We also discuss outcome. Copyright 2003, Elsevier Science (USA). All rights reserved.

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Article Outline

• Abstract

• References

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References

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Montreal Children's Hospital of the McGill University Health Center, Montreal, Quebec, Canada

☆ Address reprint requests to Hélène Flageole, MD, Montreal Children's Hospital, 2300 Tupper, Suite C-1129, Montreal, QC, Canada H3H 1P3.

PII: S1055-8586(03)70005-5

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